Amelogenesis Imperfecta

Amelogenesis imperfecta characterizes defects of the enamel resulting exclusively from genetic factors, which affect both primary and permanent dentitions. It has been suggested that the anomaly results from a defect in the enamel matrix proteins. It is mainly classified into four types according to clinical features and mode of inheritance: hypoplastic (Type I); hypomaturation (Type II); hypocalcified (Type III); and hypomaturation/hypoplasia/taurodontism (Type IV).

Amelogenesis in the Mixed Dentition